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 Formulary Chapter 9: Nutrition and blood - Full Chapter
Notes:

For enteral nutrition products, sip feeds etc see chapter 25

 Details...
09.08.01  Expand sub section  Drugs used in metabolic disorders
09.08.01  Expand sub section  Wilsons disease
09.08.01  Expand sub section  Carnitine deficiency
Levocarnitine (Carnitor)
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Restricted Drug Restricted
Red
High Cost Medicine
NHS England

NHSE commissioned for carnitine deficiency  

 
   
09.08.01  Expand sub section  Fabry's disease
09.08.01  Expand sub section  Gaucher's disease to top
09.08.01  Expand sub section  Mucopolysaccharidosis I
09.08.01  Expand sub section  Pompe disease
09.08.01  Expand sub section  Nephropathic cystinosis
Mercaptamine (cysteamine) eye drops
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Restricted Drug Restricted
Red
High Cost Medicine
NHS England

Specialist use only for nephropathic cystinosis: NHSE funded  

 
   
09.08.01  Expand sub section  Urea cycle disorders
Sodium Phenylbutyrate (Ammonaps)
Restricted Drug Restricted
Red

Hospital only – metabolic disorder 

 
   
 ....
 Non Formulary Items
Agalsidase alfa

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Non Formulary
High Cost Medicine
 
Agalsidase beta

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Non Formulary
High Cost Medicine
 
Alglucosidase Alfa  (Myozyme)

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Non Formulary
High Cost Medicine
 
Arginine

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Non Formulary
 
Asfotase alfa  (Strensiq)

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Non Formulary
 
Betaine
(Homocystinuria)

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Non Formulary
 
Biotin

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Non Formulary
 
Carglumic Acid  (Carbaglu)

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Non Formulary
High Cost Medicine
 
Chenodexoycholic acid  (Xenbilox)

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Non Formulary
 
Eliglustat  (Cerdelga)

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Non Formulary
High Cost Medicine
 
Elosulfase alfa  (Vimizim )

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Non Formulary
High Cost Medicine
 
Galsulfase  (Naglazyme)

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Non Formulary
 
Glycerol phenylbutyrate  (Ravicti)

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Non Formulary
 
Imiglucerase  (Cerezyme)

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Non Formulary
High Cost Medicine
 
Laronidase  (Aldurazyme)

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Non Formulary
High Cost Medicine
 
Mercaptamine  (Cystagon)

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Non Formulary
High Cost Medicine
 
Migalastat  (Galafold)

Non Formulary
High Cost Medicine
 
Miglustat  (Zavesca)

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Non Formulary
High Cost Medicine
 
Nitisinone

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Non Formulary
 
Penicillamine

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Non Formulary
 
Sebelipase alfa  (Kanuma)

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Non Formulary
 
Sodium Benzoate

Non Formulary
 
Sodium Dichloroacetate

Non Formulary
 
Trientine Dihydrochloride

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Non Formulary
 
Ubidecarenone

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Non Formulary

Health food supplement – see Herefordshire LPT

 

 
Zinc Acetate  (Wilzin®)

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Non Formulary
 
  
Key
note Notes
Section Title Section Title (top level)
Section Title Section Title (sub level)
First Choice Item First Choice item
Non Formulary Item Non Formulary section
Restricted Drug
Restricted Drug
Unlicensed Drug
Unlicensed
Track Changes
Display tracking information
click to search medicines.org.uk
Link to adult BNF
click to search medicines.org.uk
Link to children's BNF
click to search medicines.org.uk
Link to SPCs
SMC
Scottish Medicines Consortium
Cytotoxic Drug
Cytotoxic Drug
CD
Controlled Drug
High Cost Medicine
High Cost Medicine
Cancer Drugs Fund
Cancer Drugs Fund
NHSE
NHS England
Homecare
Homecare
CCG
CCG

Traffic Light Status Information

Status Description

Green

Suitable for use in primary care  

Amber

Specialist initiation. Shared care in place  

Red

Red do not use..  

Advice

Some formulations restricted  

Black

NICE "Do not do"  

Green 1

1st line option  

Green 2

2nd line option  

Green 3

3rd line option only  

Not Recomended / Black

Low Value Medicine not recommended for use - see NHSE guidelines  

OTC

This preparation should be bought over the counter for self-care  

Red Amber

Check product description for traffic light status  

Red Black

Low Value Medicine  

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